Primary Sjögren's syndrome with diffuse cystic lung changes developed systemic lupus erythematosus: a case report and literature review.
Identifieur interne : 000D01 ( Main/Exploration ); précédent : 000D00; suivant : 000D02Primary Sjögren's syndrome with diffuse cystic lung changes developed systemic lupus erythematosus: a case report and literature review.
Auteurs : Xiao Liu [République populaire de Chine] ; Hao Li [République populaire de Chine] ; Yunhong Yin [République populaire de Chine] ; Dedong Ma [République populaire de Chine] ; Yiqing Qu [République populaire de Chine]Source :
- Oncotarget [ 1949-2553 ] ; 2017.
Descripteurs français
- KwdFr :
- ADN (immunologie), Adulte d'âge moyen, Anticorps antinucléaires (métabolisme), Femelle, Humains, Lupus érythémateux disséminé (imagerie diagnostique), Lupus érythémateux disséminé (immunologie), Poumon (imagerie diagnostique), Syndrome de Gougerot-Sjögren (), Syndrome de Gougerot-Sjögren (diagnostic), Tomodensitométrie.
- MESH :
- diagnostic : Syndrome de Gougerot-Sjögren.
- imagerie diagnostique : Lupus érythémateux disséminé, Poumon.
- immunologie : ADN, Lupus érythémateux disséminé.
- métabolisme : Anticorps antinucléaires.
- Adulte d'âge moyen, Femelle, Humains, Syndrome de Gougerot-Sjögren, Tomodensitométrie.
English descriptors
- KwdEn :
- Antibodies, Antinuclear (metabolism), DNA (immunology), Female, Humans, Lung (diagnostic imaging), Lupus Erythematosus, Systemic (diagnostic imaging), Lupus Erythematosus, Systemic (immunology), Middle Aged, Sjogren's Syndrome (complications), Sjogren's Syndrome (diagnosis), Tomography, X-Ray Computed.
- MESH :
- chemical , immunology : DNA.
- chemical , metabolism : Antibodies, Antinuclear.
- complications : Sjogren's Syndrome.
- diagnosis : Sjogren's Syndrome.
- diagnostic imaging : Lung, Lupus Erythematosus, Systemic.
- immunology : Lupus Erythematosus, Systemic.
- Female, Humans, Middle Aged, Tomography, X-Ray Computed.
Abstract
Sjögren's syndrome (SS) is a chronic inflammatory autoimmune disease that can occur as a unique existence (primary Sjögren's syndrome) or merge with other systemic diseases like systemic lupus erythematosus (SLE), rheumatoid arthritis or systemic sclerosis (secondary Sjögren's syndrome). Data on the two diseases occurrence order are inadequate. Primary Sjögren's syndrome (pSS) may relatively uncommonly lead to diffuse cystic lung changes. We represent a female who was diagnosed pSS with diffuse cystic lung alterations developed SLE two years later. SS was diagnosed on account of the existence of dryness of eye and mouth, Schirmer's test, biopsy of the minor salivary glands of her lip, positive anti-SSA and anti-SSB antibody in the serum. Chest computed tomography image showed bilateral diffuse cystic changes with a wide variation in cyst size and distribution. SLE was finally diagnosed based on bilateral lower limb skin rash, gonarthritis and omarthritis, low level of complement, antinuclear antibody 1:640 and positive antibodies to double-stranded DNA. Improvement was achieved with therapy of corticosteroids, hydroxychloroquine and antibiotics. This report provides us clinical, diagnosis and treatment perception of SS-onset SLE as patient presenting diffuse cystic lung changes.
DOI: 10.18632/oncotarget.16010
PubMed: 28415674
Affiliations:
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Le document en format XML
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<front><div type="abstract" xml:lang="en">Sjögren's syndrome (SS) is a chronic inflammatory autoimmune disease that can occur as a unique existence (primary Sjögren's syndrome) or merge with other systemic diseases like systemic lupus erythematosus (SLE), rheumatoid arthritis or systemic sclerosis (secondary Sjögren's syndrome). Data on the two diseases occurrence order are inadequate. Primary Sjögren's syndrome (pSS) may relatively uncommonly lead to diffuse cystic lung changes. We represent a female who was diagnosed pSS with diffuse cystic lung alterations developed SLE two years later. SS was diagnosed on account of the existence of dryness of eye and mouth, Schirmer's test, biopsy of the minor salivary glands of her lip, positive anti-SSA and anti-SSB antibody in the serum. Chest computed tomography image showed bilateral diffuse cystic changes with a wide variation in cyst size and distribution. SLE was finally diagnosed based on bilateral lower limb skin rash, gonarthritis and omarthritis, low level of complement, antinuclear antibody 1:640 and positive antibodies to double-stranded DNA. Improvement was achieved with therapy of corticosteroids, hydroxychloroquine and antibiotics. This report provides us clinical, diagnosis and treatment perception of SS-onset SLE as patient presenting diffuse cystic lung changes.</div>
</front>
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